We describe a female, 44-year-old, with asynptomatic polyostticfibrous dysplasia (PFD). She showed non cafè-au-lait nevi and no endocrine dysfunction. Nosological confusion may exist between PFD and McCune-Albright Syndrome (MAS). PFD often occurs alone, while MAS is characterized by PFD, patchy skin pigmentation and multiple endocrinopaties. These two conditions represent the same disease with variable expression.
Displasia fibrosa poliostotica. Late onset-polyostotic fibrous dysplasia: Pathogenetic considerations
SANGUINETI, FRANCESCA;
1993-01-01
Abstract
We describe a female, 44-year-old, with asynptomatic polyostticfibrous dysplasia (PFD). She showed non cafè-au-lait nevi and no endocrine dysfunction. Nosological confusion may exist between PFD and McCune-Albright Syndrome (MAS). PFD often occurs alone, while MAS is characterized by PFD, patchy skin pigmentation and multiple endocrinopaties. These two conditions represent the same disease with variable expression.
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