Sfoglia per Autore
Time -dependent normalization of defective Slex expression and GDP-mannose 4,6 dehydratase (GMD) activity in long-term culture of lymphocytes from a LAD II patients.
1999-01-01 Tonetti, Michela; Sturla, Laura; Bisso, A; Zanardi, D; DE FLORA, Antonio; Etzioni, A.
Structural and enzymatic characterization of human recombinant GDP-D-mannose 4,6 dehydratase
1999-01-01 Bisso, A.; Sturla, Laura; Zanardi, D.; DE FLORA, A.; Tonetti, Michela
Probing the catalytic mechanism of GDP-4-keto-6-deoxy-D-mannose epimerase/reductase by kinetic and crystallographic characterization of site specific mutants
2000-01-01 Rosano, C; Bisso, A; Izzo, G; Tonetti, Michela; Sturla, Laura; DE FLORA, A; Bolognesi, M.
Impairment of the Golgi GDP-L-fucose transport and unresponsiveness to fucose replacement therapy in LAD II patients
2000-01-01 Sturla, Laura; Puglielli, L; Tonetti, Michela; Berninsone, P; Etzioni, A; Hirschberg, C.
The high resolution structure of GDP-4-keto-6-deoxy-D-mannose epimerase/reductase.
2000-01-01 Rosano, C; Izzo, G; Sturla, Laura; Bisso, A; Tonetti, Michela; Bolognesi, M.
Effect of defective import of GDP-fucose into Golgi apparatus on glycoconjugates composition in cells from LAD II patient
2001-01-01 Sturla, Laura; Bisso, A; Zanardi, D; Tonetti, Michela
Impairment of the Golgi GDP-L-fucose transport and unresponsiveness to fucose replacement therapy in LAD II patients
2001-01-01 Sturla, Laura; Puglielli, L.; Tonetti, Michela; Bernisone, P.; Hirschberg, C.; DE FLORA, A.; Etzioni, A.
Kinetic and Crystallographic Analises Support a Sequential-ordered Bi Bi Catalytic Mechanism for Escherichia Coli Glucose-1-Thymidyltransferase.
2001-01-01 Zuccotti, S.; Zanardi, D.; Rosano, C.; Sturla, Laura; Tonetti, Michela; Bolognesi, M.
Equilibrative and concentrative nucleoside transporters mediate influx of extracellular cyclic ADP-ribose into 3T3 murine fibroblasts
2002-01-01 Guida, Lucrezia; Bruzzone, Santina; Sturla, Laura; Franco, L.; Zocchi, Elena; DE FLORA, Antonio
Characterization of the residual fucose-containing glycoconjugates in LAD II/CDGS IIc cells
2002-01-01 Sturla, L; Rampal, R; Haltiwanger, Rs; Zanardi, D; Etzioni, A; Tonetti, Michela
The chlorella virus PBCV-1 encodes two enzymes involved in the de novo synthesis of GDP-L-fucose.
2002-01-01 Tonetti, Michela; Zanardi, D; Gurnon, J; Sturla, Laura; Damonte, Gianluca; Van Etten, J.
Cloning and expression of two enzymes involved in the de novo synthesis of GDP-L-fucose in PBCV-1
2002-01-01 Tonetti, Michela; Sturla, Laura; Zanardi, D; Fruscione, Floriana; Damonte, Gianluca; Van Etten, J.
Analisi strutturale degli oligosaccaridi N-linked e O-linked contenenti fucoso nelle glicoproteine di pazienti affetti da sindrome LAD II
2002-01-01 Sturla, Laura; Zanardi, D; Haltiwanger, Rs; Tonetti, Michela
Equilibrative and concentrative nucleoside transporters mediate the influx of Cyclic ADP-ribose into 3T3 murine fibroblasts.
2002-01-01 Guida, Lucrezia; Bruzzone, Santina; Zocchi, Elena; Sturla, Laura; Franco, L; DE FLORA, Antonio
Leukocyte adhesion deficiency (LAD) type II/carbohydrate deficient glycoprotein (CDG)IIc-founder effect and genotype/phenotype correlation
2002-01-01 Etzioni, A.; Sturla, Laura; Antonellis, A.; Green, E. D.; GERSHONI BARUCH, R.; Bernisone, P. M.; Hirschberg, C. B.; Tonetti, Michela
Differential terminal fucosylation of N-Linked glycans versus protein O-Fucosylation in Leukocyte Adhesion Deficiency Type II (CDG IIc)
2003-01-01 Sturla, Laura; Rampal, R; Haltiwanger, Rs; Fruscione, Floriana; Etzioni, A; Tonetti, Michela
The Chlorella virus PBCV-1 encodes two enzymes involved in the de novo synthesis of GDP-L-fucose and GDP-D-rhamnose
2003-01-01 Fruscione, Floriana; Tonetti, Michela; Zanardi, D; Gurnon, Jr; Armirotti, A; Damonte, Gianluca; Sturla, Laura; De Flora, A. Van Etten J. L.
Inibizione selettiva della cicloossigenasi-2 attraverso l’utilizzo di acidi peptidil nucleici in macrofagi murini
2003-01-01 Scarfi', Sonia; Giovine, Marco; Millo, Enrico; Clavarino, E; Pozzolini, Marina; Sturla, Laura; Benatti, Umberto; Damonte, Gianluca
A model for biosilification studies: primorphs from the marine sponge Petrosia ficiformis and molecular cloning of silicatein gene
2003-01-01 Pozzolini, Marina; Sturla, Laura; Cerrano, Carlo; Bavestrello, Giorgio; Camardella, L; Parodi, A; Benatti, Umberto; Giovine, Marco
Differential terminal fucosylation of N-Linked glycans versus protein O-Fucosylation in Leukocyte Adhesion Deficiency Type II (CDG IIc).
2003-01-01 Sturla, Laura; Rampal, R; Haltiwanger, Rs; Zanardi, D; Etzioni, A; Tonetti, Michela
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