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A minimal isoform of the TMEM16A protein associated with chloride channel activity 1-gen-2011 Ferrera, L; Scudieri, P; Sondo, Elvira; Caputo, A; Caci, E; Zegarra Moran, O; Ravazzolo, Roberto; Galietta, Lj
The anoctamin family: TMEM16A and TMEM16B as calcium-activated chloride channels 1-gen-2012 Scudieri, P.; Sondo, E.; Ferrera, L.; Galietta, L. J. V.
Association of TMEM16A chloride channel overexpression with airway goblet cell metaplasia 1-gen-2012 Scudieri, P; Caci, E; Bruno, Silvia; Ferrera, L; Schiavon, M; Sondo, Elvira; Tomati, V; Gianotti, Ambra; Zegarra Moran, O; Pedemonte, N; Rea, Francesco; Ravazzolo, Roberto; Galietta, Lj
Epithelial sodium channel silencing as a strategy to correct the airway surface fluid deficit in cystic fibrosis 1-gen-2013 Gianotti, Ambra; Melani, R; Caci, E; Sondo, Elvira; Ravazzolo, Roberto; Galietta, Lj; Zegarra Moran, O.
TMEM16A-TMEM16B chimaeras to investigate the structure-function relationship of calcium-activated chloride channels 1-gen-2013 Scudieri, P; Sondo, Elvira; Caci, E; Ravazzolo, Roberto; Galietta, Lj
Non-canonical translation start sites in the TMEM16A chloride channel 1-gen-2014 Sondo, Elvira; Scudieri, P; Tomati, V; Caci, E; Mazzone, A; Farrugia, G; Ravazzolo, Roberto; Galietta, Lj
Upregulation of TMEM16A protein in bronchial epithelial cells by bacterial pyocyanin 1-gen-2015 Caci, Emanuela; Scudieri, Paolo; Carlo, Emma Di; Morelli, Patrizia; Bruno, Silvia; De Fino, Ida; Bragonzi, Alessandra; Gianotti, Ambra; Sondo, Elvira; Ferrera, Loretta; Palleschi, Alessandro; Santambrogio, Luigi; Ravazzolo, Roberto; Galietta, Luis J. V.
Ion channel and lipid scramblase activity associated with expression of TMEM16F/ANO6 isoforms 1-gen-2015 Scudieri, Paolo; Caci, Emanuela; Venturini, Arianna; Sondo, Elvira; Pianigiani, Giulia; Marchetti, Carla; Ravazzolo, Roberto; Pagani, Franco; Galietta, Luis J. V.
Genetic Inhibition of the Ubiquitin Ligase Rnf5 Attenuates Phenotypes Associated to F508del Cystic Fibrosis Mutation 1-gen-2015 Tomati, Valeria; Sondo, Elvira; Armirotti, Andrea; Caci, Emanuela; Pesce, Emanuela; Marini, Monica; Gianotti, Ambra; Ju Jeon, Young; Cilli, Michele; Pistorio, Angela; Mastracci, Luca; Ravazzolo, Roberto; Scholte, Bob; Ronai, Ze'Ev; Galietta, Luis J. V.; Pedemonte, Nicoletta
High-throughput screening identifies FAU protein as a regulator of mutant cystic fibrosis transmembrane conductance regulator channel 1-gen-2018 Tomati, V.; Pesce, E.; Caci, E.; Sondo, E.; Scudieri, P.; Marini, M.; Amato, F.; Castaldo, G.; Ravazzolo, R.; Galietta, L. J. V.; Pedemonte, N.
The Autophagy Inhibitor Spautin-1 Antagonizes Rescue of Mutant CFTR Through an Autophagy-Independent and USP13-Mediated Mechanism 1-gen-2018 Pesce, Emanuela; Sondo, Elvira; Ferrera, Loretta; Tomati, Valeria; Caci, Emanuela; Scudieri, Paolo; Musante, Ilaria; Renda, Mario; Baatallah, Nesrine; Servel, Nathalie; Hinzpeter, Alexandre; di Bernardo, Diego; Pedemonte, Nicoletta; Galietta, Luis J V
Discovery of a picomolar potency pharmacological corrector of the mutant CFTR chloride channel 1-gen-2020 Pedemonte, N.; Bertozzi, F.; Caci, E.; Sorana, F.; Fruscia, P. D.; Tomati, V.; Ferrera, L.; Rodriguez-Gimeno, A.; Berti, F.; Pesce, E.; Sondo, E.; Gianotti, A.; Scudieri, P.; Bandiera, T.; Galietta, L. J. V.
Partial rescue of f508del-cftr stability and trafficking defects by double corrector treatment 1-gen-2021 Capurro, V.; Tomati, V.; Sondo, E.; Renda, M.; Borrelli, A.; Pastorino, C.; Guidone, D.; Venturini, A.; Giraudo, A.; Bertozzi, S. M.; Musante, I.; Bertozzi, F.; Bandiera, T.; Zara, F.; Galietta, L. J. V.; Pedemonte, N.
Rescue by elexacaftor-tezacaftor-ivacaftor of the G1244E cystic fibrosis mutation's stability and gating defects are dependent on cell background 1-gen-2022 Tomati, Valeria; Costa, Stefano; Capurro, Valeria; Pesce, Emanuela; Pastorino, Cristina; Lena, Mariateresa; Sondo, Elvira; Di Duca, Marco; Cresta, Federico; Cristadoro, Simona; Zara, Federico; Galietta, Luis J V; Bocciardi, Renata; Castellani, Carlo; Lucanto, Maria Cristina; Pedemonte, Nicoletta
The L467F-F508del Complex Allele Hampers Pharmacological Rescue of Mutant CFTR by Elexacaftor/Tezacaftor/Ivacaftor in Cystic Fibrosis Patients: The Value of the Ex Vivo Nasal Epithelial Model to Address Non-Responders to CFTR-Modulating Drugs 1-gen-2022 Sondo, E.; Cresta, F.; Pastorino, C.; Tomati, V.; Capurro, V.; Pesce, E.; Lena, M.; Iacomino, M.; Baffico, A. M.; Coviello, D.; Bandiera, T.; Zara, F.; Galietta, L. J. V.; Bocciardi, R.; Castellani, C.; Pedemonte, N.
Targeting of Ubiquitin E3 Ligase RNF5 as a Novel Therapeutic Strategy in Neuroectodermal Tumors 1-gen-2022 Principi, E.; Sondo, E.; Bianchi, G.; Ravera, S.; Morini, M.; Tomati, V.; Pastorino, C.; Zara, F.; Bruno, C.; Eva, A.; Pedemonte, N.; Raffaghello, L.
Mostrati risultati da 1 a 16 di 16
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